Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

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Gigantiform cementoma – Wikipedia

Apart from typical multiquadrant and expansile abnormalies involving both jaws, he also suffered from several times of fractures in lower extremity. A The adolescent patient with a huge mass extending along the mandible body. All teeth posterior to the first primary molar were absent, owing to previous extractions, and the remaining tooth germs were displaced.

A 6-year-old female presented with a main complaint of a painless maxillary swelling which her parents noticed 8 months earlier. Dentistry stubs Rare cancers. A The adolescent patient’s aunt who had received surgery nonvascularized iliac bone reconstruction 30 years ago now complaint of anterior maxillary mass with chronic infection.

His previous surgical history was remarkable and extensive.

Clinical Synopsis Toggle Dropdown. While the OMIM database is open to the public, users seeking information about a personal medical or genetic condition are urged to consult with a qualified physician for diagnosis and for answers to personal questions.

Gigantiform cementoma

By clicking accept or continuing to use the site, you agree to the terms outlined in our Privacy PolicyTerms of Serviceand Dataset License. Therefore, we agree with Noffke et al 14 and Finical 15 in resorting to a complete resection of FGC with curative purposes whenever feasible.


Abstract Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion.

Periprosthetic bone mineral density changes after unicondylar knee arthroplasty. To keep both practitioners and patients informed of the overall bony changes and corresponding risks of fractures, we contended that DEA should be routinely tested since initial clinic visit. They observed the disorder in a mother, 2 of her daughters, and a son.

D Postoperative view of patient after bilateral mandibulectomy. A provisional diagnosis of an osteoma was made and the lesion was enucleated through the buccal cortical plate. Infected lesions and those presenting with progressive expansion ecmentoma generally removed surgically through enucleation.

The sharp contrast of CT images between densely bony deposits in FGC lesion and the radiolucent low-density images confirmed our hypothesis that both maxilla and mandible of FGC shared unevenly and favorable distribution of calcium deposits in the general calcium metabolism of whole body. In concurrence with the boy and his parent’s wishes, we decided to perform a bilateral segmental mandibulectomy and to tentatively reconstruct the corresponding defect with vascularized iliac bone flaps.

Open in a separate window. Medunsa CampusSouth Africa. This article has been cited by other articles in PMC. The objective of this report is to present an unusual case of a gigantiform cementoma manifesting with gross expansion of the maxilla in a 6-year-old black female. December Learn how and giganttiform to remove this template message. Author information Article notes Copyright and License information Disclaimer.

Familial Gigantiform Cementoma

Case report A 6-year-old female presented with a main complaint of a painless maxillary swelling which her parents noticed 8 months earlier.

As a direct consequence, physical deterioration was also found by his parents.


Gardner’s Syndrome — the importance of early diagnosis: J Neurosurg Pediatr ; 7: E Postoperative panorex X-ray showed vascularized iliac bone flap for reconstruction. She was yet no exception given her own narratives of femur fracture during adolescence.

West Indian Med J ; Misfortunes and troubles never come singly. Out of the group of lesions categorized as ODs, only FGC presents clinically with significant jaw expansion. Showing of 15 references.

A year-old male patient was referred to our hospital for recurrence of a huge benign tumor in oral cavity.

Expert curators review the literature and gigantiforrm it to facilitate your work. Apart from that, it is still debatable about the timing of surgical intervention for FGC patients. Dentomaxillofac Radiol ; During the rapid growth phase of FGC in cementma and maxilla, the other bones, especially long bones in lower extremities, were simultaneously undergoing a calcium absorption or transportation problem, as was reflected in the osteoporotic radiographic changes in our adolescent patient.

Autosomal dominant gigantiform cementoma associated with bone fractures.

The radiolucent peripheral margin showed cellular fibrous connective tissue with psammomatoid and trabecular bony deposits. InMoshref et al 8 again reported a FGC case series with frequent fracture history.

Familial Gigantiform Cementoma

Autosomal cementlma gigantiform cementoma associated with bone fractures. The radiographic evaluations of lower limb revealed decreased bone density and thinner- or void-cortex structures around fracture regions. Fibro-osseous lesions of the head and neck.